Spinal arteriovenous malformations associated with Klippel-Trenaunay-Weber syndrome: a literature search and report of two cases.
نویسندگان
چکیده
SUMMARY Patients with Klippel-Trenaunay-Weber syndrome present with venous varices, cutaneous capillary malformations, and tissue hypertrophy, usually involving an extremity. A small but important subset also harbors arteriovenous malformations (AVMs) of the spine. We report 2 such cases, 1 with 3 concurrent spinal arteriovenous fistulas. These cases and our review of the literature emphasize the importance of screening the spine for AVMs. In addition, it is also important to investigate for the presence of multiple spinal AVMs.
منابع مشابه
Parkes Weber syndrome and spinal arteriovenous malformations.
We read with great interest the article written by Alomari et al, and agree with the authors that Klippel-Trenaunay syndrome is not associated with spinal cord AVM. However, in their discussion, in relationship to spinal cord AVM with Parkes Weber syndrome, they comment briefly that “Spinal AVM has not been reported to be a feature of Parkes Weber syndrome.” Here, we demonstrate a case of Parke...
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ورودعنوان ژورنال:
- AJNR. American journal of neuroradiology
دوره 28 3 شماره
صفحات -
تاریخ انتشار 2007